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From Doctor Koop

 

When Mark and Angie King's daughter Erica was born, she seemed perfectly healthy. She was alert. She babbled. She smiled when she saw them. There were no signs to warn them that something might be wrong, the Celina, Ohio, parents recall. But six months later, Mark King began to suspect Erica couldn't hear. He

noticed he had to tap her before she'd turn to face him. Angie King refused to believe there might be a problem.  "Sometimes when we walked into the room, she'd look. Sometimes she wouldn't," Angie King says. "I dismissed it."  When Erica was 9 months old, Angie King grew alarmed when her babbling and cooing dropped off. So the Kings took her to an audiologist, who diagnosed that she was deaf. Of the 4 million babies born in the United States each year, about 12,000 are born deaf, according to the Deafness Research Foundation in Washington D.C. But the condition is no longer the soundless sentence it used to be.  "If we could catch every baby who is deaf at birth, we can enable almost every one of them to hear" to some extent, says Jack Wheeler, the deafness foundation's president and CEO. "If you don't have your baby tested at birth, you are not going to know your baby is deaf until it's almost too late."

If deafness is diagnosed early enough, experts say, most children who are born that way can have at least some hearing restored through technological improvements like high‑powered digital hearing aids and cochlear implants, which are mechanical devices that produce digitally coded electrical signals transmitted directly to the auditory system. But time is critical. Deaf infants' brains begin to adapt almost immediately to the lack of auditory input, according to Dr. Calvin Sia, a physician at the Hawaii State School for the Deaf and Blind and a member of the American Academy of Pediatrics' Task Force on Newborn and Infant Hearing.

 

Permanent damage by age 3

By age 3, permanent damage occurs. The longer a child goes without hearing, the more difficult it will be to ever learn language in the same way hearing children learn, Sia says. And many children's hearing loss is being discovered dangerously late, when they are, on average, 22 years old, Wheeler adds. There are two commonly used methods for testing infants. The first is an auditory brain‑stem response, in which sensors are placed on the head and neck to detect levels of brain activity in response to sound. The second, an otoacoustic emissions test, uses a soft rubber probe placed within the ear canal to measure the ear's response to stimulus. Each test costs between $35 and $50.  Yet only about 35 percent of infants are tested in American hospitals, Wheeler says.

"There is a clock that's ticking in the baby's brain," he adds. "New parents must insist on having your baby's hearing tested in the birthing hospital. Don't take 'no' for an answer."  However, not all doctors believe that testing every child is necessary, or even practical.  Part of the problem is money, according to Dr. Paul Kileny, director of the audiology and electrophysiology department at the University of Michigan Health System. Kileny says states with mandated hearing tests failed to make sure that doctors and hospitals would get paid for the testing.  Kileny himself favors testing only those infants who have at least one risk factor: low birth weight, a family history of childhood deafness; are infected with a virus such as herpes; need an antibiotic, respirator or heart‑lung

machine after birth; or have abnormalities of the head, face or neck.

About 4 percent to 6 percent of infants with those risk factors will have a hearing loss, compared to only 0.5 percent of infants without any risk factors, Kileny says  Second, he says, some children born with the ability to hear lose their hearing when they are several months old, so the money would be better spent teaching pediatricians to spot signs of hearing loss.

       But to the parents of deaf children, testing every child seems absolutely worthwhile.  Once she was diagnosed, Erica King, who is now 4, used hearing aids before recently receiving a cochlear implant And when the Kings' second daughter was born, they refused to leave the

hospital before she was tested. Jaime, now 2 years old, was also born deaf.

       She is now using hearing aids. "There was nothing that would alert us there was something wrong," Angie King says. "It is very deceptive. You can't tell by clapping your hands or banging pots and pans. All children need to be tested."  Approximately 30 states now have laws requiring that infants get tested for hearing loss before they leave the hospital.  But the success of such programs varies widely, according to the deafness foundation, because not all the states have earmarked the necessary funds for the programs and the tests. In a recently issued report card on each state's success rate in instituting universal screening, the foundation found:  Those states that scored "excellent" (almost all babies are screened and a statewide system of coordination, training, quality assurance and follow‑up has been established) included: Colorado, Connecticut, Hawaii, Iowa, Mississippi, New Mexico, Rhode Island and Wyoming.  Marked unsatisfactory were places in which fewer than 15 percent of babies are screened and there is no governmental effort or coordination. They included: Alaska, Indiana, Nebraska, New Hampshire, New York, Vermont, Washington state and Puerto Rico. For More Information,

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